Interlink of Two Syndromes - Demarquay-van der Woude and Popliteal Pterygium in One Family Group

Although Demarquay first described the Fistula labia inferioris congenua in 1845, Van der Woude  reviewed these features and established a relationship between lower lip pits and cleft lip or palate. Demarquay-van derWoude Syndrome (DVWS) (OMIM 119300) is an autosomal dominant condition that affects embryologic facial development and is characterized by the usual two labial pits (fistulae) or elevations in the lower lip, cleft lip with or without cleft palate. 
Dental agenesis is seldom. Lip pits or sinuses are usually symmetrically and bilaterally located on the vermilion portion of the lower lip on either side of the midline. They are less unilaterally, medially or bilaterally asymmetrical. 

The sinuses penetrate the orbicularis oris muscle and mostly communicate with the underlying minor salivary glands, and are usually asymptomatic with intermittent or continuous drainage of watery or salivary secretions. Hypotonia of the muscles of the lower lip has also been described in DVWS, leading some authors to suggest the existence of real central lip dysplasia. Read more>>>>>>>>>














Comments

Post a Comment

Popular posts from this blog

Harvesting Free Palatal Masticatory Mucosal Graft Using 3a Mucotome

Image
The technique of free autogenous gingival grafting (FGG) has undergone little modification since its introduction by Bjorn in Scandinavia in 1963 and by King and Pennel inthe United States in 1964. The technique is widely used to treat a variety of mucogingival problems such as insufficient or lack of attached gingiva, the presence of high frenum attachments, shallow fornix and denuded roots following gingival recession.  FGG can be procured from donor site using scalpels, gingivectomy knife or palatal shaving knife (Paquette knife). The donor site is frequently the palate, although the use of edentulous ridge areas, tuberosity and attached gingiva has also been described. Scalpel is most commonly used and conventional method for procuring gingival auto grafts. Gingivectomy knife, although not commonly used, also works on similar principle. Since the scalpel blade is straight and stiff and the palate is curved, repeated incisions to release the graft from underlying conn...
Read more

Indications for Orthognathic Surgery

Image
Orthognathic surgery (OS) is a surgical intervention that alters relationships of the jaws and dental arches. The treatment involves a combination of orthodontics and maxillofacial surgery.  Orthognathic Surgery It is used to correct dentofacial deformities that cannot be treated with acceptable results by conventional orthodontics. The first description of a surgical intervention to correct a malocclusion was by Hullihen in 1849. The most frequently used surgical procedures for correcting the relationship of the jaws are Le Fort I osteotomy and sagittal ramus split osteotomy. Also often used are vertical ramus osteotomy, inverted L osteotomy, and variations and combinations of the above. Read More>>>>>>
Read more

Micro-Implant Anchorage for Orthodontic Treatment of Bialveolar Protrusion

Image
Conventional methods of reinforcing orthodontic anchorage have several disadvantages, including complicated appliance design and the need for exceptional patient cooperation. Kanomi and Costa et al.   introduced the use of titanium microscrews and miniscrews for orthodontic anchorage. Microscrews are small enough to place in any area of the alveolar bone, easy to implant and remove, and inexpensive.    In addition, orthodontic force application can begin almost immediately after implantation. In particular, microscrews have been shown to produce en masse retraction of the six anterior teeth. So it was decided to use micro-implants to treat a patient having Class 1 bialveolar protrusion where anchorage demands are critical. The patient, a 15-year-old female, had a convex profile and a Class I skeletal pattern with bialveolar protrusion Cephalometric analysis showed an ANB angle of 4°, a mandibular plane angle (FMA) of 20° and facial angle of 88°. Read more>...
Read more